Sunday, December 21, 2008

kikuchi disease

This rare disease is also known as necrotizing histiocytic lymphadenitis or Kikiuch Fujimoto disease. Most commonly presented as non-specific tender posterior cervical lymph adenitis. It has been linked to infectiouse as well as autoimmune etiology. The expansion occurs pericortically in LN, with apoptotic CD123+ plamacytoid monocytes (same as SLE). It has been treated with steroids, immunoglobulins as well as antibiotics.

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